天主教耕莘醫院新店總院 外科部 泌尿科
Bilateral adrenal tumor related to multiple endocrine neoplasia type 2
Meng-Che Chiang, Bing-Juin Chiang, Chun-Hou Liao
Division of Urology, Department of Surgery, Cardinal Tien Hospital and
Fu-Jen Catholic University, Taipei, Taiwan
Bilateral adrenal tumors are very rare in clinical practice. To differential diagnosis of bilateral adrenal tumor is also challenging.
A 29 year old man suffered from hypertension for over 2 years but with poor response to medical control. Incidental findings of thyroid nodule and bilateral adrenal tumor during health check up. Hyperparathyroidism was also reported after examination. Patient then received bilateral laparoscopic adrenalectomy.
Multiple Endocrine Neoplasia type IIa (MEN IIa) an autosomal dominant syndrome characterized by pheochromocytoma, medullary thyroid carcinoma and hyperparathyroidism. Pheochromocytoma occurs in approximately 50% of patients with MEN IIa.
Hereditary pheochromocytoma should be kept in mild for patient with bilateral adrenal tumor. The association with MENII is also known. Further check up for thyroid, parathyroid function of patient and family should be considered.