高雄榮民總醫院 外科部 泌尿科；義大醫院病理部
Rare case report-pelvic ganglioneuroma
Mon-Der Cho1、Chia-Cheng Yu1、Hao Wen Chuang2、Tong-Lin Wu1
Division of Urology, Department of Surgery Kaohsiung Veterans General hospital1; Department of Pathology EDA Hospital, Kaohsiung, Taiwan2
Ganglioneuroma is a rare and benign tumor of the autonomic nerve fibers arising from neural crest sympathogonia, which are completely undifferentiated cells of the sympathetic nervous system. However, ganglioneuromas themselves are fully differentiated neuronal tumors that do not contain immature elements. Ganglioneuromas most frequently occur in the abdomen, however these tumors can grow anywhere sympathetic nervous tissue is found. Other common locations include the adrenal gland, paraspinal retroperitoneum, posterior mediastinum, head, and neck. We would like to present a 17 years old female with a huge pelvic mass extent to right upper quadrant of abdomen size measures in 21x5.4x8.5 CM. Debulking surgery was performed and revealed a huge ganglioneuroma of retroperitoenum, the clinical presentation, special image and pathological picture and our experience in management of huge retroperitoneal tumor with literature review.