Renal hemangioblastoma: an unusual case
腎血管母細胞瘤：一個罕見的案例分享
Cheng Chia-Wei、Tsai Yuh-Shyan
鄭嘉緯、蔡育賢
Department of Urology, National Cheng Kung University Hospital, College of Medicine, Tainan, Taiwan
國立成功大學醫學院附設醫院泌尿部
Renal hemangioblastoma is an uncommon tumor that can occur sporadically and viewed as a benign entity. Thus, we reported this tumor in a 47-year-old Taiwanese male case, Hepatitis B virus carrier, whom was incidentally found via abdominal computed tomography. There was no flank pain or hematuria complained. Abdominal sonography showed one hyperechoic nodule (22mm) located at the upper pole of left kidney, mimic with angiomyolipoma. Both of CT and MRI demonstrated moderate enhancement. The RENAL score was 5.
Left retroperitoneal laparoscopic partial nephrectomy was performed uneventfully with warm ischemia time of 12 minutes. Histologically, the cellular portion was composed of a rich capillary network of single-layered flat endothelial cells enclosing stromal cells, and the paucicellular portion contained hyalinized stroma which are positive for alpha-inhibin and NSE but negative for CK, CD68, CD34, HMB-45 and STAT-6. Although renal hemangioblastoma is rare and difficult
to be diagnosed, it cannot be neglected at all and required more cases for the further study.