卓孟德¹、余家政¹、莊豪文²、吳東霖¹

高雄榮民總醫院 外科部 泌尿科；義大醫院病理部

Mon-Der Cho¹、Chia-Cheng Yu¹、Hao Wen Chuang²、Tong-Lin Wu¹

Division of Urology, Department of Surgery Kaohsiung Veterans General hospital¹; Department of Pathology EDA Hospital, Kaohsiung, Taiwan²

 

Ganglioneuroma is a rare and benign tumor of the autonomic nerve fibers arising from neural crest sympathogonia, which are completely undifferentiated cells of the sympathetic nervous system. However, ganglioneuromas themselves are fully differentiated neuronal tumors that do not contain immature elements. Ganglioneuromas most frequently occur in the abdomen, however these tumors can grow anywhere sympathetic nervous tissue is found. Other common locations include the adrenal gland, paraspinal retroperitoneum, posterior mediastinum, head, and neck. We would like to present a 17 years old female with a huge pelvic mass extent to right upper quadrant of abdomen size measures in 21x5.4x8.5 CM. Debulking surgery was performed and revealed a huge ganglioneuroma  of retroperitoenum, the clinical presentation, special image and pathological picture and our experience in management of huge retroperitoneal tumor with literature review.