張朋暉¹、林宜佳^1,2、黃一勝^1,2

新光吳火獅紀念醫院 外科部 泌尿科¹

輔仁大學 醫學系²

Peng-Hui Chang¹, Yi-Chia Lin^1,2, Chao-Yen Ho¹, Te-Fu Tsai^1,2, Thomas I.S. Hwang^1,2

Division of Urology, Department of Surgery, Shin Kong WHS Memorial Hospital¹

School of Medicine, Fu-Jen Catholic University²

 

Paraganglioma, also known as extra-adrenal pheochromocytoma, is a rare seen catecholamines-secreting neuroendocrine tumor. Excessive secretion of catecholamine cause nonspecific symptoms and signs such as headache, episodic sudden perspiration, and tachycardia. One of the common sites of extra-adrenal pheochromocytoma is organ of Zuckerkandl. Herein, we report a 61 years-old female who came to our hospital with occasional palpitation and hot flush. Intermittent hypertension was noted, too. A computed tomography scan with contrast showed a left infra-renal tumor with obstructive uropathy and involving organ of Zuckerkandl. Further lab study showed increased in only dopamine level. Her epinephrine and nor-epinephrine were within normal range. Robotic-assisted retroperitoneal tumor excision was done uneventfully. The pathology study proved the functional extra-adrenal paraganglioma. The patient did not experience further palpitation and hot flush after operation. Follow-up computed tomography showed no recurrence or metastasis and her dopamine level returned to normal. The literatures were reviewed and discussed.