良性腎臟血管平滑肌脂肪瘤合併腎靜脈及下腔靜脈血栓: 病例報告及文獻回顧
戴大堯、蔡育賢
國立成功大學附設醫院 泌尿部
Benign renal angiomyolipoma with renal vein and inferior vena cava thrombosis: a case report with review of literature
Ta-Yao Tai, Yuh-Shyan Tsai
Department of Urology, College medicine and Hospital, National Cheng Kung University, Tainan, Taiwan
Renal angiomyolipoma (AML) is thought to derive from perivascular epithelioid cell. It is the most common benign mesenchymal neoplasm of the kidney, which is composed of fat cells, smooth muscle cells, and thick-wall blood vessels. Conversely to classic type AML, epithelioid AML presence of an epithelioid cell component, has a malignancy tendency. To our knowledge, classic type AML seldom presented with extension to renal vein or vena cava. In this present case report, we describes an incidentally diagnosed right renal mass in a 55-year-old man. CT scan showed a well-defined hypodense mass lesion about 9 cm in size in the upper pole of the right kidney, with invasive to right renal vein and inferior vena cava. The patient received right radical nephrectomy and thrombectomy of inferior vena cava. The pathology confirmed the classic angiomyolipoma with caval thrombosis.
Due to the rarity of classic angiomyolipoma with venous thrombosis, herein we also reviewed the literature in terms of imaging features, treatment strategy and prognosis.